Colon perforation in a patient with hyperimmunoglobulin E (Job's) syndrome

Chen, Chung-Ming; Lai, Hong-Shiee; Lin, Chern-Long; Hsieh, Kue-Shiung

« Previous Next »Journal of Pediatric Surgery
Volume 30, Issue 10 , Pages 1479-1480, October 1995

Colon perforation in a patient with hyperimmunoglobulin E (Job's) syndrome

Chung-Ming Chen
- Department of Surgery, National Taiwan University Hospital, Taipei, Taiwan, Republic of China.
- Department of Pediatrics, National Taiwan University Hospital, Taipei, Taiwan, Republic of China.
Hong-Shiee Lai
- Address reprint requests to Hong-Shiee Lai, MD, Department of Surgery, National Taiwan University Hospital, No. 7, Chung-Shan South Rd, Taipei, Taiwan, Republic of China.
- Department of Surgery, National Taiwan University Hospital, Taipei, Taiwan, Republic of China.
- Department of Pediatrics, National Taiwan University Hospital, Taipei, Taiwan, Republic of China.
Chern-Long Lin
- Department of Surgery, National Taiwan University Hospital, Taipei, Taiwan, Republic of China.
- Department of Pediatrics, National Taiwan University Hospital, Taipei, Taiwan, Republic of China.
Kue-Shiung Hsieh
- Department of Surgery, National Taiwan University Hospital, Taipei, Taiwan, Republic of China.
- Department of Pediatrics, National Taiwan University Hospital, Taipei, Taiwan, Republic of China.

Abstract

A Taiwanese boy was diagnosed as having hyperimmunoglobulin E syndrome at the age of 4 years. At age 18 he was admitted to the hospital because of pneumonia in the left lower lobe. Abdominal pain developed 9 days later, and his condition progressed to peritonitis. Colon perforation, 10 cm distal to the ileocecal valve, was found. Double-barrel ileostomy was performed, and reanastomosis was done later. Afterward, he was fine, and he had no significant gastrointestinal problems after being discharged. To the authors' knowledge, this is the first reported case of hyperimmunoglobulin E syndrome complicated by colon perforation.