Hirschsprung's disease associated with Ondine's curse: A special subgroup?
Abstract
The authors report a case of the rare concurrence of congenital central hypoventilation syndrome (Ondine's curse) and long segmental colonic aganglionosis (Hirschsprung's disease). A review of 24 reported cases showed that the proportion of females having this concurrence is higher than for ordinary Hirschsprung's disease. It also appears that the aganglionic segment is much longer in these cases than in ordinary Hirschsprung's disease.
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aDepartment of Pediatric Surgery, University of Tokyo, Tokyo, Japan.
bthe Department of Pediatrics, Toshima Metropolitan Hospital, Tokyo, Japan.
Address reprint requests to Yoshiaki Tsuchida, MD, Department of Pediatric Surgery, University of Tokyo, 7-3-1 Hongo, Bunkyo-ku, Tokyo 113, Japan.
ABSTRACT