Journal of Pediatric Surgery
Volume 31, Issue 6 , Pages 809-811, June 1996

Multiple entero-entero fistulae: An unusual complication of Henoch-Schönlein purpura

  • Kenneth W. Gow

      Affiliations

    • Department of Surgery, British Columbia's Children's Hospital, Vancouver, British ColumbiaCanada.
    • Department of Pathology, British Columbia's Children's Hospital, Vancouver, British ColumbiaCanada.
    • Department of Pediatrics, British Columbia's Children's Hospital, Vancouver, British ColumbiaCanada.
    • the University of British Columbia, Vancouver, British ColumbiaCanada.
  • ,
  • James J. Murphy III

      Affiliations

    • Corresponding Author InformationAddress reprint requests to Dr James J. Murphy, British Columbia's Children's Hospital, Room A242B-4480 Oak St, Vancouver, British Columbia, Canada V6H 3V4.
    • Department of Surgery, British Columbia's Children's Hospital, Vancouver, British ColumbiaCanada.
    • Department of Pathology, British Columbia's Children's Hospital, Vancouver, British ColumbiaCanada.
    • Department of Pediatrics, British Columbia's Children's Hospital, Vancouver, British ColumbiaCanada.
    • the University of British Columbia, Vancouver, British ColumbiaCanada.
  • ,
  • Geoffrey K. Blair

      Affiliations

    • Department of Surgery, British Columbia's Children's Hospital, Vancouver, British ColumbiaCanada.
    • Department of Pathology, British Columbia's Children's Hospital, Vancouver, British ColumbiaCanada.
    • Department of Pediatrics, British Columbia's Children's Hospital, Vancouver, British ColumbiaCanada.
    • the University of British Columbia, Vancouver, British ColumbiaCanada.
  • ,
  • James Fergal Magee

      Affiliations

    • Department of Surgery, British Columbia's Children's Hospital, Vancouver, British ColumbiaCanada.
    • Department of Pathology, British Columbia's Children's Hospital, Vancouver, British ColumbiaCanada.
    • Department of Pediatrics, British Columbia's Children's Hospital, Vancouver, British ColumbiaCanada.
    • the University of British Columbia, Vancouver, British ColumbiaCanada.
  • ,
  • Jane Hailey

      Affiliations

    • Department of Surgery, British Columbia's Children's Hospital, Vancouver, British ColumbiaCanada.
    • Department of Pathology, British Columbia's Children's Hospital, Vancouver, British ColumbiaCanada.
    • Department of Pediatrics, British Columbia's Children's Hospital, Vancouver, British ColumbiaCanada.
    • the University of British Columbia, Vancouver, British ColumbiaCanada.

Abstract 

Henoch-Schönlein purpura (HSP) is an immunologically mediated systemic vasculitis of small blood vessels that frequently involves the gastrointestinal tract. Surgeons often are asked to assess patients with HSP for abdominal pain. Common complications that lead to surgical intervention include intussusception, perforation, necrosis, and massive gastrointestinal bleeding. However, the development of multiple entero-entero fistulae has not been described previously. Herein the authors describe the case of a 10-year-old girl with HSP who had a typical rash, seizures secondary to central nervous vasculitis, and gastrointestinal involvement. The abdominal pain persisted for several days until marked fever and hypotension developed, which necessitated surgical intervention. During laparotomy, multiple entero-entero fistulae of the ileum were found, which required resection and primary anastomosis. Histological examination of the ileum was consistent with HSP vasculitis. The patient made an unremarkable recovery and has had no recurrence of symptems.

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 Presented at the 27th Annual Meeting of the Canadian Association of Paediatric Surgeons, Montreal, Quebec, September 2–4, 1995.

PII: S0022-3468(96)90139-6

Journal of Pediatric Surgery
Volume 31, Issue 6 , Pages 809-811, June 1996