Abstract
A 13-month-old girl presented with a large malignant rhabdoid liver tumor that ruptured
soon after admission. Six years after an emergency right hepatectomy and subsequent
chemotherapy (ifosfamide, vincristine, and actinomycin D), she remains well and disease
free. Previously, these rare tumors invariably have been fatal and resistant to multimodal
therapy. This is the first report of long-term survival of a patient with a malignant
rhabdoid liver tumor. J Pediatr Surg 37:1488-1490. Copyright 2002, Elsevier Science (USA). All rights reserved.
Keywords
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Article info
Footnotes
☆Address reprint requests to M.D. Stringer, MS, FRCS, Children's Liver Centre, Gledhow Wing, St James's University Hospital, Leeds LS9 7TF, England.
Identification
Copyright
© 2002 Published by Elsevier Inc.
