Abstract
This report describes a case of a term male 3.1 kg, normal delivery, 38 weeks of gestation
with a record of hydramnios by prenatal sonography. He had fetal acute suffering and
respiratory distress. The first radiographic study showed a mass filling the whole
left thorax cage causing erosion of the inferior edge of the third rib. The mediastinum
was displaced to the right. Computed tomography scan confirmed a homogeneous tumor
that filled the left thorax and displaced the mediastinum to the right without invasion.
Surgical biopsy informed of a highly vascularized mesenchymal tumor. The tumor was
embolized with Ivalon microparticles obtaining a nearly avascular mass. Complete surgical
excision was made, including the whole mass and costal segments. Microscopically,
it was an inflammatory myofibroblastic tumor. It was composed mainly of spindle-shaped
cells without malignant features. On immunohistochemistry, the tumor showed positive
staining for vimentin, whereas antidesmin antibodies and S-100 protein were negative.
The aim of this article is to present an extremely uncommon case of neonatal distress
caused by an intrathoracic, extrapulmonary myofibroblastic tumor. Complete surgical
resection was possible after embolization.
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References
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© 2005 Elsevier Inc. Published by Elsevier Inc. All rights reserved.
