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Bannayan-Zonana syndrome is a rare disorder characterized by macrocephaly and multiple
soft tissue and visceral hamartomas. This report presents a sporadic patient with
macrocephaly, lipomas, hemangiomas, and lymphangiomas who died of cardiac and respiratory
failure due to progressive cervicomediastinal arteriovenous fistulous hemangiomas
at the age of 9 years.
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References
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- Macrocephaly, pseudopapilledema, and multiple hemangiomata: A previously undescribed heredofamilial syndrome.Pediatrics. 1960; 26: 293-300
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Article info
Footnotes
*Presented at the 24th Annual Meeting of the Pacific Association of Pediatric Surgeons, Hong Kong, May 20–24, 1991.
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Copyright
© 1992 W.B. Saunders Company. All right reserved. Published by Elsevier Inc.
