Rapid Communication| Volume 41, ISSUE 6, e11-e13, June 2006

Duodenojejunal atresia with absent dorsal mesentery, choledochal cyst, and malrotation in a premature newborn—a case report


      We present the case of a premature baby who was born with the following conditions: an extensive atresia from the first part of the duodenum to the mid small bowel; malrotation of the distal part, in volvulus and in an “apple peel” configuration; no connection of the bile ducts to the bowel; and presence of a type II choledochal cyst. To our knowledge, this is the first case in which a combination of these anomalies is reported. A brief review of the relevant literature is also presented.

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