We present the case of a premature baby who was born with the following conditions: an extensive atresia from the first part of the duodenum to the mid small bowel; malrotation of the distal part, in volvulus and in an “apple peel” configuration; no connection of the bile ducts to the bowel; and presence of a type II choledochal cyst. To our knowledge, this is the first case in which a combination of these anomalies is reported. A brief review of the relevant literature is also presented.
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- Familial combined duodenal and jejunal atresia.J Pediatr Surg. 1996; 31: 1573
- Intestinal atresia and stenosis. A 25-year experience with 277 cases.Arch Surg. 1998; 133: 490-496
- Multiple hereditary gastrointestinal atresias: study of a family.Acta Paediatr Scand. 1983; 72: 773-777
- Is there an association between duodenal atresia and choledochal cyst?.J Pediatr Gastroenterol Nutr. 2005; 40: 378-381
- Choledochal cyst and duodenal atresia: a rare combination of malformations.Pediatr Surg Int. 2004; 20: 724-726
- Duodeno-jejunal atresia with volvulus, absent dorsal mesentery, and absent superior mesenteric artery: a hereditary compound structure in duodenal atresia?.Am J Med Genet. 2002; 109: 52-55
- A 13q- syndrome with extensive intestinal atresia.Acta Paediatr Scand. 1985; 74: 305-308
- Duodenal and jejunal atresia with agenesis of the dorsal mesentery: “apple peel” small bowel.Am J Surg. 1979; 137: 676-678
- Apple peel small bowel: an uncommon variant of duodenal and jejunal atresia.J Pediatr Surg. 1970; 5: 595-600
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