Abstract
We present the case of a premature baby who was born with the following conditions:
an extensive atresia from the first part of the duodenum to the mid small bowel; malrotation
of the distal part, in volvulus and in an “apple peel” configuration; no connection
of the bile ducts to the bowel; and presence of a type II choledochal cyst. To our
knowledge, this is the first case in which a combination of these anomalies is reported.
A brief review of the relevant literature is also presented.
Index words
To read this article in full you will need to make a payment
Purchase one-time access:
Academic & Personal: 24 hour online accessCorporate R&D Professionals: 24 hour online accessOne-time access price info
- For academic or personal research use, select 'Academic and Personal'
- For corporate R&D use, select 'Corporate R&D Professionals'
Subscribe:
Subscribe to Journal of Pediatric SurgeryAlready a print subscriber? Claim online access
Already an online subscriber? Sign in
Register: Create an account
Institutional Access: Sign in to ScienceDirect
References
- Familial combined duodenal and jejunal atresia.J Pediatr Surg. 1996; 31: 1573
- Intestinal atresia and stenosis. A 25-year experience with 277 cases.Arch Surg. 1998; 133: 490-496
- Multiple hereditary gastrointestinal atresias: study of a family.Acta Paediatr Scand. 1983; 72: 773-777
- Is there an association between duodenal atresia and choledochal cyst?.J Pediatr Gastroenterol Nutr. 2005; 40: 378-381
- Choledochal cyst and duodenal atresia: a rare combination of malformations.Pediatr Surg Int. 2004; 20: 724-726
- Duodeno-jejunal atresia with volvulus, absent dorsal mesentery, and absent superior mesenteric artery: a hereditary compound structure in duodenal atresia?.Am J Med Genet. 2002; 109: 52-55
- A 13q- syndrome with extensive intestinal atresia.Acta Paediatr Scand. 1985; 74: 305-308
- Duodenal and jejunal atresia with agenesis of the dorsal mesentery: “apple peel” small bowel.Am J Surg. 1979; 137: 676-678
- Apple peel small bowel: an uncommon variant of duodenal and jejunal atresia.J Pediatr Surg. 1970; 5: 595-600
Article info
Identification
Copyright
© 2006 Elsevier Inc. Published by Elsevier Inc. All rights reserved.
