Abstract
Esophageal atresia (EA) with or without tracheoesophageal fistula (TEF) is a relatively
common congenital condition in which there have been several described anatomical
variants. The most common type, EA with distal TEF, comprises more than 75% of cases
in many reports. Less commonly, a smaller proximal pouch fistula (H-type) will be
associated with this most common variant in 1.4% of these cases. Only 2% of all cases
of EA/TEF will have 2 large fistulas between the trachea and esophagus in which the
end of the upper esophageal pouch connects terminally to the midtrachea and the distal
esophagus arises from the trachea near the carina. Here we describe the management
of an infant with this type of EA/TEF who was also found to have an H-type TEF of
the proximal trachea. The combination of this type of EA/TEF with an associated H-type
TEF or “triple fistula” has been previously described in the literature in only 1
other patient.
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References
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© 2007 Elsevier Inc. Published by Elsevier Inc. All rights reserved.
