Abstract
Congenital pouch colon syndrome is partial or complete replacement of the colon by
a pouch-like structure and anorectal malformation. Commonly reported from northern
India, we believe this is the first report of congenital pouch colon syndrome in a
Saudi Arabian neonate. He was referred with an imperforate anus and diagnosed as having
a high anorectal malformation. The patient underwent a sigmoid colostomy. Continued
abdominal distension after the colostomy prompted sonography and computed tomography,
which showed an air- and fluid-containing cystic structure in the abdomen. Exploration
revealed a thick-walled cystic structure in continuity with the distal colostomy and
with a blood supply mainly from the superior mesenteric artery. The ureters were dilated
and tortuous and the pouch opened into the posterior vesical wall. The pouch was resected
and an end colostomy fashioned. The etiopathogenesis classification and management
of the congenital pouch colon syndrome are discussed.
Index words
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Article info
Publication history
Accepted:
August 22,
2007
Received in revised form:
August 22,
2007
Received:
July 26,
2007
Identification
Copyright
© 2008 Elsevier Inc. Published by Elsevier Inc. All rights reserved.
