Rapid Communication| Volume 43, ISSUE 8, e37-e40, August 2008

An unusual case of female hypospadias associated with a pelvic mass


      Female hypospadias is a rare malformation. We report on an unusual case that presented with a urethral dimple in the perineum in association with a pelvic soft tissue sarcoma compressing and displacing the urethra. The diagnosis was made by cystoscopy, and, as the patients remained asymptomatic, no treatment was eventually required for her urologic malformation. This is, to our knowledge, the first reported case of female hypospadias associated with a perineal urethral dimple. The possible pathogenesis of the malformation is discussed also in relation to the simultaneous presence of a pelvic mass.

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        • Knight H.M.L.
        • Philiphs N.J.
        • Mouriquand P.D.E.
        Female hypospadias: a case report.
        J Paediatr Surg. 1995; 30: 1738-1740
        • Currarino G.
        Large prostatic utricles and related structures, urogenital sinus and other forms of urethrovaginal confluence.
        J Urol. 1986; l36: 1270-1279
        • Stephens F.D.
        Congenital intrinsic lesions of the female urethra.
        in: Stephens F.D. Congenital malformations of the urinary tract. Praeger, New York1983: 150-158
        • Ruymann F.B.
        • Maddux H.R.
        • Ragab A.
        • et al.
        Congenital anomalies associated with rhabdomyosarcoma: an autopsy study of 115 cases. A report from the Intergroup Rhabdomyosarcoma Study Committee Group.
        Med Pediatr Oncol. 1988; 16: 33-39
        • Cope J.U.
        • Tsokos M.
        • Helman L.J.
        • et al.
        Inguinal hernia in patients with Ewing sarcoma: a clue to etiology.
        Med Pediatr Oncol. 2000; 34: 195-199
        • Hurwitz R.S.
        • Fitzpatrick T.J.
        Vaginal urethra, clitoridal hypertrophy and accessory phallic urethra: a rare syndrome of female pseudohermaphroditism.
        J Urol. 1982; l27: 1165-1168
        • Gonzales R.
        Reconstruction of the female urethra to allow intermittent catheterization for neurogenic bladders and urogenital sinus anomalies.
        J Urol. 1985; l33: 478-480
        • Hendren W.H.
        Reconstructive problems of the vagina and the female urethra.
        Clin Plast Surg. 1981; 7: 207-234
        • Hensle T.W.
        • Crooks K.K.
        Urethral reconstruction in the young female using a perineal pedicle flap.
        J Pediatr Surg. 1982; 17: 687-694
        • Wadie B.S.
        • ElHifnawy A.
        • Khair A.A.
        Reconstruction of female urethra: versatility, complexity and aptness.
        J Urol. 2007; 177: 2205-2210