Abstract
Congenital cystic adenomatoid malformation, a rare developmental, hamartomatous abnormality
of the lung, usually is unilateral, is localized, and presents in early infancy. Delayed
occurrence in older children and multilobar involvement are rare. We describe a case
of congenital cystic adenomatoid malformation type 1 with multilobar involvement,
associated emphysema, and coexistent tracheobronchopathia osteochondroplastica in
an adolescent girl for whom the correct diagnosis was achieved only on histologic
examination. The importance of an accurate diagnosis of this entity enables proper
subtyping, management to minimize the risk of infections and malignancy, and exclusion
of associated malformations.
Key words
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Article info
Publication history
Accepted:
November 18,
2009
Received in revised form:
November 18,
2009
Received:
August 12,
2009
Identification
Copyright
© 2010 Elsevier Inc. Published by Elsevier Inc. All rights reserved.
