Abstract
Localized myopathy of the muscular layers may be an important factor contributing
to segmental dilatation of the intestine (SDI). Only one report has described SDI
of the jejunum in a neonate showing no abnormality of the interstitial cells of Cajal
(ICC). The present report describes the very rare case of a neonatal girl with segmental
dilatation of the distal duodenum and proximal jejunum with irregular arrangements
of Auerbach's plexus and ICC and the successful surgical treatment of SDI. We review
the literature on this type of relationship between abnormality of ICC and SDI and
discuss the clinical features of this complication. Furthermore, the possible neuropathic
cause of SDI complicated with disorders of ICC was explored in this report.
Key words
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References
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Article info
Publication history
Accepted:
March 22,
2010
Received in revised form:
March 21,
2010
Received:
September 17,
2009
Footnotes
☆This study was not supported by any grants.
Identification
Copyright
© 2010 Elsevier Inc. Published by Elsevier Inc. All rights reserved.
