Abstract
Systemic polyarteritis nodosa (PAN) is a rare disease in childhood affecting small
and midsized arteries. The typical presentation in children is of isolated 1- or 2-organ
involvement, and the diagnosis is often based on the histopathology. We report a case
of pediatric PAN whose presenting symptom was jejunal obstruction owing to ischemic
necrosis of the small bowel. The postoperative recovery was uneventful, and the patient
responded well to steroid therapy. There are only a few cases of PAN with intestinal
involvement described in the literature, some of them fatal. The diagnosis of PAN
should be considered in children with acute intestinal obstruction with no obvious
etiology, as early recognition and treatment may reduce its high mortality.
Key words
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References
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Article info
Publication history
Accepted:
March 25,
2011
Received in revised form:
January 25,
2011
Received:
June 10,
2010
Identification
Copyright
© 2011 Elsevier Inc. Published by Elsevier Inc. All rights reserved.
