Abstract
Pulmonary sequestration is an uncommon congenital malformation of the lung that can
be classified as intralobar or extralobar (ELS). Approximately 90% of ELS occur in
the left hemithorax. Approximately 10% of ELS may present below the diaphragm. Both
types of sequestrations are characterized by pulmonary tissue that does not communicate
with the bronchial tree. The arterial blood supply to 80% ELS is through a direct
branch of the thoracic or abdominal aorta, in 15% via another systemic artery and
5% from the pulmonary artery. The venous drainage of ELS is variable, predominantly
into the systemic circulation (via the azygos vein, hemiazygos vein, or inferior vena
cava). Approximately 25% drain completely or partially through the pulmonary veins.
We report an extremely rare case of ELS with unusual venous drainage to the portal
vein.
Key words
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References
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Article info
Publication history
Accepted:
November 27,
2011
Received in revised form:
November 6,
2011
Received:
September 18,
2011
Identification
Copyright
© 2012 Elsevier Inc. Published by Elsevier Inc. All rights reserved.
