Abstract
Bronchopulmonary foregut malformation (BPFM) is a group of rare congenital anomalies
that affect the respiratory and upper gastrointestinal tracts. We report here the
first case of prenatal depiction of communicating BPFM, including extrapulmonary sequestration
and foregut cyst, both with pancreatic differentiation. Magnetic resonance imaging
on the fetus confirmed a polymalformative syndrome with right-lung and gastric cysts
and allowed the detection of respiratory and alimentary tracts communication and aberrant
feeding vessels. Diagnosis was confirmed after birth by multidetector computed tomography
and postnatal pathologic findings. The patient, a boy, underwent surgery for respiratory
distress at 4 weeks of life. This singular case confirms the benefits of early surgery
for communicating BPFM.
Key words
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Article info
Publication history
Accepted:
December 16,
2011
Received:
November 30,
2011
Identification
Copyright
© 2012 Elsevier Inc. Published by Elsevier Inc. All rights reserved.
