Abstract
We report the complex case of a 12-month-old girl with stage IV hepatoblastoma accompanied
by thrombosis and cavernous transformation of the portal vein. After neoadjuvant chemotherapy,
she underwent right hepatectomy, which was complicated by iatrogenic injury of her
left hepatic duct, and subsequently developed a postoperative biloma and chronic biliocutaneous
fistula. Concomitant with multiple percutaneous interventions to manage the biloma
nonoperatively while the child completed her adjuvant chemotherapy, she progressed
to develop chronic malnutrition, jaundice, and failure to thrive. Once therapy was
completed and the child was deemed free of disease, she underwent exploratory laparotomy
with Roux-en-Y biliary cystenterostomy for definitive management, resulting in resolution
of her biliary fistula, jaundice, and marked improvement in her nutritional status.
Roux-en-Y biliary cystenterostomy is a unique and efficacious management option in
the highly selected patient population with chronic biliary leak refractory to minimally
invasive management.
Key words
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References
- Liver tumors in children.Oncologist. 2008; 13: 812-820
- Tumors of the liver in children.Surg Oncol. 2007; 16: 195-203
- Guidelines for surgical treatment of hepatoblastoma in the modern era—recommendations from the Childhood Liver Tumour Strategy Group of the International Society of Paediatric Oncology (SIOPEL).Eur J Cancer. 2005; 41: 1031-1036
- The current management of hepatoblastoma: a combination of chemotherapy, conventional resection, and liver transplantation.J Pediatr. 2005; 146: 204-211
- Outcome and complications after resection of hepatoblastoma.J Pediatr Surg. 2004; 39 ([discussion 199-202]): 199-202
- Surgical view of the treatment of patients with hepatoblastoma: results from the first prospective trial of the International Society of Pediatric Oncology Liver Tumor Study Group.Cancer. 2002; 94: 1111-1120
- Surgical treatment of hepatic tumors in children: lessons learned from liver transplantation.J Pediatr Surg. 2009; 44: 2083-2087
- Cisplatin, doxorubicin, and delayed surgery for childhood hepatoblastoma: a successful approach—results of the first prospective study of the International Society of Pediatric Oncology.J Clin Oncol. 2000; 18: 3819-3828
- Bile leakage after hepatic resection.Ann Surg. 2001; 233: 45-50
- Risk factors and management of bile leakage after hepatic resection.World J Surg. 2003; 27: 695-698
- Biliary complications after hepatic resection: risk factors, management, and outcome.Arch Surg. 1998; 133: 156-161
- Bile leakage and liver resection: where is the risk?.Arch Surg. 2006; 141 ([discussion 695]): 690-694
- Surgical injury of the biliary tract in children.Eur J Pediatr Surg. 2000; 10: 100-105
- Successful treatment of intrahepatic biloma by combined percutaneous and endoscopic technique: an intrabiloma “rendezvous”.Gastrointest Endosc. 2006; 63: 721-723
- Utility of ERCP in neonatal and infant cholestasis.J Laparoendosc Adv Surg Tech A. 2009; 19: 431-436
- Surgical management and long-term follow-up of patients with choledochal cysts.Am J Surg. 1993; 165: 238-242
- Congenital bile duct cysts: classification, operative procedures, and review of thirty-seven cases including cancer arising from choledochal cyst.Am J Surg. 1977; 134: 263-269
- Pancreaticobiliary maljunction.Clin Gastroenterol Hepatol. 2009; 7: S84-88
- Surgical treatment of hepatic hydatidosis.Schweiz Med Wochenschr. 1991; 121: 1231-1237
- “The fate” of a peri-cystic-jejunostomy in the treatment of the hydatid liver cysts.Chirurgia (Bucur). 2006; 101: 81-82
- Internal intestinal drainage for postoperative biloma in a patient with biliary atresia.Japanese Journal of Pediatric Surgery. 2002; 34: 1426-1429
- Operative and nonoperative management of pancreatic pseudocysts.Surg Clin North Am. 2007; 87 ([ix]): 1447-1460
Article info
Publication history
Accepted:
June 8,
2012
Received in revised form:
June 7,
2012
Received:
March 19,
2012
Footnotes
☆Conflict of interests statement: The authors have no conflicts of interest to report.
Identification
Copyright
© 2012 Elsevier Inc. Published by Elsevier Inc. All rights reserved.