Abstract
Ehlers-Danlos syndrome type IV, also known as the vascular type, is the most severe
form of the disease. It may cause spontaneous bowel perforation and rupture of major
arteries. The treatment of bowel perforation in this population remains controversial
because they are at risk for major wound complications owing to poor healing. We report
the first use of laparoscopy in children with Ehlers-Danlos syndrome.
Key words
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References
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Article info
Publication history
Accepted:
June 8,
2012
Received in revised form:
May 8,
2012
Received:
February 22,
2012
Identification
Copyright
© 2012 Elsevier Inc. Published by Elsevier Inc. All rights reserved.
