Abstract
Pulmonary venous malformation is extremely rare. We present imaging and clinical findings
of a 17-year-old male with multifocal subcutaneous venous malformations and multiple
cystic lesions in the liver and spleen, suggestive of slow flow vascular malformation.
In the right lung, chest radiography followed by chest CT demonstrated large tortuous
pulmonary veins and cystic emphysematous changes. Tc99m-MAA (pertechnetate-labeled
macroaggregated albumin) lung perfusion scan demonstrated only 3% of normal perfusion
to the right lung, with no evidence of arteriovenous shunting. The child had diffuse
intraparenchymal hemorrhage throughout the right lower and middle lobes and underwent
resection. Pathology confirmed the diagnosis of venous malformation complicated with
bleeding.
Key words
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References
Enjolras O., Wassef M. and Chapot R. Color atlas of vascular tumors and vascular malformations. Cambridge University Press.
- Pulmonary venous malformation in a 4-year-old boy: a case report.Korean J Radiol. 2009; 10: 420-423
- Classification and imaging of vascular malformations in children.Eur Radiol. 2003; 13: 2483-2497
- Vascular low-flow malformations in children: current concepts for classification, diagnosis and therapy.Eur J Radiol. 2005; 53: 35-45
- Pulmonary manifestations in Proteus syndrome: pulmonary varicosities and bullous lung disease.Am J Med Genet A. 2011; 155: 865-869
- Pulmonary arteriovenous malformations a state of the art review..Am J Respir Crit Care Med. 1998; 158: 643-661
- Venous malformation: classification, development, diagnosis and interventional radiologic management.Radiol Clin North Am. 2008; 46: 545-597
Article info
Publication history
Accepted:
September 12,
2012
Received in revised form:
September 12,
2012
Received:
June 15,
2012
Identification
Copyright
© 2012 Elsevier Inc. Published by Elsevier Inc. All rights reserved.
