Abstract
We describe a case of congenital extensive central venous thrombosis presenting as
polyhydramnios and massive ascites, requiring amnioreduction prenatally and refractory
chylous ascites and chylothoraces postnatally. Echocardiography, computed tomography
angiogram (CTA), and magnetic resonance venogram (MRV) were helpful in defining the
nature and extent of the lesion. The patient underwent staged procedures of repeated
abdominal paracentesis, chest drain insertion, and right internal jugular vein exploration
initially. Subsequently, open thromboembolectomy from the upper venous system veins
and pericardial patch angioplasty of the right internal jugular and right innominate
veins were required and managed by catheter-directed thrombolysis for the residual
thrombosis with successful recovery.
Key words
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Article info
Publication history
Accepted:
November 13,
2012
Received in revised form:
November 6,
2012
Received:
August 10,
2012
Identification
Copyright
© 2013 Elsevier Inc. Published by Elsevier Inc. All rights reserved.
