Abstract
The absence of extrahepatic portal bifurcation is a rare anomaly and is considered
to be caused by anomalous development of the portal vessels early in fetal life. The
portal system develops from two main fetal vessels, the left umbilical vein and right
vitelline vein. An anomalous connection of these two vessels early in fetal life results
in the absence of bifurcation of the portal vein. We report a case who suffered from
biliary atresia complicated with the absence of bifurcation of the portal vein. The
patient had an anomalous left hepatic portal vein that ran along the cranial side
of the hepatic hilar ductal plate. This is the first report of biliary atresia that
was complicated with the absence of extrahepatic portal bifurcation.
Key words
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Article info
Publication history
Accepted:
December 8,
2012
Received in revised form:
November 20,
2012
Received:
August 28,
2012
Identification
Copyright
© 2013 Elsevier Inc. Published by Elsevier Inc. All rights reserved.
