Abstract
Pancreatoblastoma is a rare pancreatic tumor that is most commonly encountered in
infants and young children. This report describes an unusual presentation of a large
pancreatic body pancreatoblastoma presenting with intraabdominal bleeding due to spontaneous
rupture of the tumor in a 5-year-old boy. Subsequent molecular analysis from the resected
specimen identified a mutation in CTNNB1 and aberrant methylation of the tumor suppressor RASSF1A.
Key words
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Article info
Publication history
Accepted:
February 5,
2013
Received in revised form:
February 2,
2013
Received:
November 5,
2012
Footnotes
☆This study was not supported by any grants.
☆☆Conflict of interest and financial support: The authors who have taken part in this study declare that they do not have anything to disclose regarding funding or any conflict of interest with respect to this manuscript.
Identification
Copyright
© 2013 Elsevier Inc. Published by Elsevier Inc. All rights reserved.
