Abstract
Management of pediatric patients with pheochromocytomas associated with genetic syndromes,
such as Von Hippel-Lindau (VHL) disease, is complex owing to the need for continuous
surveillance, high rates of recurrence, multiple operations during childhood, and
the possibility of lifelong exogenous steroid replacement. We report the successful
treatment of two siblings with VHL who underwent a total of six cortical-sparing procedures
without requiring steroid therapy.
Key words
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Article info
Publication history
Accepted:
April 3,
2013
Received in revised form:
April 2,
2013
Received:
December 31,
2012
Footnotes
☆Disclosures: The authors have no disclosures or sources of support to report with respect to the preparation of this manuscript.
Identification
Copyright
© 2013 Elsevier Inc. Published by Elsevier Inc. All rights reserved.
