Extrarenal Wilms tumor: a case report and review of the literature


      Extrarenal Wilms tumors are extremely rare with only isolated case reports in the pediatric literature. We present the case of a 2-year old boy who presented with a large abdominal mass and constipation. Pathologic diagnosis of the tumor was extrarenal Wilms tumor (ERWT) with favorable histology. We discuss the diagnostic workup, radiologic and operative findings, treatment and review of the literature.

      Key words

      To read this article in full you will need to make a payment

      Purchase one-time access:

      Academic & Personal: 24 hour online accessCorporate R&D Professionals: 24 hour online access
      One-time access price info
      • For academic or personal research use, select 'Academic and Personal'
      • For corporate R&D use, select 'Corporate R&D Professionals'


      Subscribe to Journal of Pediatric Surgery
      Already a print subscriber? Claim online access
      Already an online subscriber? Sign in
      Institutional Access: Sign in to ScienceDirect


        • D'Angio G.J.
        The National Wilms Tumor Study: a 40 year perspective.
        Lifetime Data Anal. 2007; 13: 463-470
        • Davidoff A.M.
        Wilms tumor.
        Adv Pediatr. 2012; 59: 247-267
        • Deshpande A.V.
        • Gawali J.S.
        • Sanghani H.H.
        • et al.
        Extrarenal Wilm's tumour — a rare entity.
        Pediatr Surg Int. 2002; 18: 543-544
        • Zhang D.Y.
        • Lin T.
        • Wei G.H.
        • et al.
        A rare case of simultaneous occurrence of Wilms' tumor in the left kidney and the bladder.
        Pediatr Surg Int. 2010; 26: 319-322
        • Armanda V.
        • Culic S.
        • Pogorelic Z.
        • et al.
        Rare localization of extrarenal nephroblastoma in 1-month-old female infant.
        J Pediatr Urol. 2012; 8: e43-e45
        • Yamamoto T.
        • Nishizawa S.
        • Ogiso Y.
        Paratesticular extrarenal Wilms' tumor.
        Int J Urol. 2012; 19: 490-491
        • Arda I.S.
        • Tuzun M.
        • Demirhan B.
        • et al.
        Lumbosacral extrarenal Wilms' tumour: a case report and literature review.
        Eur J Pediatr. 2001; 160: 617-619
        • Hiradfar M.
        • Shojaeian R.
        • Zabolinejad N.
        • et al.
        Extrarenal Wilms' tumour presenting as an inguinal mass.
        Arch Dis Child. 2012; 97: 1077
        • Oner U.U.
        • Tokar B.
        • Acikalin M.F.
        • et al.
        Wilms' tumor of the ovary: a case report.
        J Pediatr Surg. 2002; 37: 127-129
        • Taguchi S.
        • Shono T.
        • Mori D.
        • et al.
        Extrarenal Wilms tumor in children with unfavorable histology: a case report.
        J Pediatr Surg. 2010; 45: e19-e22
        • Govender D.
        • Hadley G.P.
        • Nadvi S.S.
        • et al.
        Primary lumbosacral Wilms tumour associated with occult spinal dysraphism.
        Virchows Arch. 2000; 436: 502-505
        • Abrahams J.M.
        • Pawel B.R.
        • Duhaime A.C.
        • et al.
        Extrarenal nephroblastic proliferation in spinal dysraphism. A report of 4 cases.
        Pediatr Neurosurg. 1999; 31: 40-44
        • Andrews P.E.
        • Kelalis P.P.
        • Hasse G.M.
        Extrarenal Wilms’ tumor: results of the National Wilms Tumor Study.
        J Pediatr Surg. 1992; 27: 1181-1184
        • Orlowski J.P.
        • Levin H.S.
        • Dyment P.G.
        Intrascrotal Wilms' tumor developing in a heterotopic renal anlage of probable mesonephric origin.
        J Pediatr Surg. 1980; 15: 679-682
        • Aterman K.
        Extrarenal nephroblastomas.
        J Cancer Res Clin Oncol. 1989; 115: 409-417
        • Song J.S.
        • Kim I.K.
        • Kim Y.M.
        • et al.
        Extrarenal teratoid Wilms' tumor: two cases in unusual locations, one associated with elevated serum AFP.
        Pathol Int. 2010; 60: 35-41
        • Chowhan A.K.
        • Reddy M.K.
        • Javvadi V.
        • et al.
        Extrarenal teratoid Wilms' tumour.
        Singapore Med J. 2011; 52: e134-e137