Fetal primary small bowel volvulus in a child without intestinal malrotation

  • Jae Hee Chung
    Corresponding author. Department of Pediatric Surgery, St. Mary's Hospital, The Catholic University of Korea, Youngdeungpo-gu, Seoul 150–713, Korea. Tel.: +82 2 3779 1031, +82 11 255 2980; fax: +82 2 786 0802.
    Department of Surgery, Yeouido St' Mary's Hospital, The Catholic University of Korea, Seoul, South Korea
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  • Gye-Yeon Lim
    Department of Radiology, Yeouido St' Mary's Hospital, The Catholic University of Korea, Seoul, South Korea
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  • Ji Sun We
    Department of Obstetrics and Gynecology, Yeouido St' Mary's Hospital, The Catholic University of Korea, Seoul, South Korea
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      Fetal primary small bowel volvulus without atresia or malrotation is an extremely rare but life-threatening surgical emergency. We report a case of primary small bowel volvulus that presented as sudden fetal distress and was diagnosed on the basis of the ‘whirl-pool sign’ of fetal sonography. This diagnosis led to emergency operation after birth at the third trimester with a good outcome. Although the pathogenesis of fetal primary small bowel volvulus is unclear, ganglion cell immaturity may play a role in the etiology.

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