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Peliosis hepatis in a child with myotubular myopathy: Successful treatment using hepatic artery embolization

  • Joseph P. Terlizzi
    Correspondence
    Corresponding Author. Department of Surgery, University of Medicine and Dentistry of New Jersey- Robert Wood Johnson Medical School, One Robert Wood Johnson Way, New Brunswick, NJ 08903, USA.
    Affiliations
    Department of Surgery, University of Medicine and Dentistry of New Jersey- Robert Wood Johnson Medical School, One Robert Wood Johnson Way, New Brunswick, NJ 08903, USA
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  • Robert Azizi
    Affiliations
    Department of Radiology, University of Medicine and Dentistry of New Jersey- Robert Wood Johnson Medical School, One Robert Wood Johnson Way, New Brunswick, NJ 08903, USA
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  • Monica D. Chow
    Affiliations
    Department of Surgery, University of Medicine and Dentistry of New Jersey- Robert Wood Johnson Medical School, One Robert Wood Johnson Way, New Brunswick, NJ 08903, USA
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  • Sharon Underberg-Davis
    Affiliations
    Department of Radiology, University of Medicine and Dentistry of New Jersey- Robert Wood Johnson Medical School, One Robert Wood Johnson Way, New Brunswick, NJ 08903, USA
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  • John L. Nosher
    Affiliations
    Department of Radiology, University of Medicine and Dentistry of New Jersey- Robert Wood Johnson Medical School, One Robert Wood Johnson Way, New Brunswick, NJ 08903, USA
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  • Perry W. Stafford
    Affiliations
    Department of Pediatric Surgery, University of Medicine and Dentistry of New Jersey- Robert Wood Johnson Medical School, One Robert Wood Johnson Way, New Brunswick, NJ 08903, USA
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  • Joelle Pierre
    Affiliations
    Department of Pediatric Surgery, University of Medicine and Dentistry of New Jersey- Robert Wood Johnson Medical School, One Robert Wood Johnson Way, New Brunswick, NJ 08903, USA
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      Abstract

      Peliosis hepatis (PH) is a rare condition characterized by multiple blood-filled spaces within the hepatic parenchyma that can lead to fatal hemorrhage. There is no consensus on the best treatment algorithm for PH, and therapy is directed at removing the potential causative agent with operative intervention when necessary. Here we present the first known case of PH in a child with myotubular myopathy who was successfully treated with angiography and hepatic artery embolization as a first line therapy, without the need for operative intervention. Awareness of this condition and the available treatment modalities may lead to favorable outcomes in future cases.

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