Advertisement
Case report| Volume 33, ISSUE 4, P666-667, April 1998

Congenital short bowel syndrome associated with appendiceal agenesis and functional intestinal obstruction

  • Nuvit Sarimurat
    Correspondence
    Address reprint requests to Nuvit Sarimurat, MD, Istanbul Evleri Koza 10 Daire 15, Bahcelievler-İstanbul, Turkey.
    Affiliations
    Department of Paediatric Surgery, Cerrahpasa Medical Faculty, University of İstanbul, İstanbul, Turkey

    Department of Pathology, Cerrahpasa Medical Faculty, University of İstanbul, İstanbul, Turkey.
    Search for articles by this author
  • Sinan Celayir
    Affiliations
    Department of Paediatric Surgery, Cerrahpasa Medical Faculty, University of İstanbul, İstanbul, Turkey

    Department of Pathology, Cerrahpasa Medical Faculty, University of İstanbul, İstanbul, Turkey.
    Search for articles by this author
  • Mehmet Elicevik
    Affiliations
    Department of Paediatric Surgery, Cerrahpasa Medical Faculty, University of İstanbul, İstanbul, Turkey

    Department of Pathology, Cerrahpasa Medical Faculty, University of İstanbul, İstanbul, Turkey.
    Search for articles by this author
  • Sergulen Dervisoglu
    Affiliations
    Department of Paediatric Surgery, Cerrahpasa Medical Faculty, University of İstanbul, İstanbul, Turkey

    Department of Pathology, Cerrahpasa Medical Faculty, University of İstanbul, İstanbul, Turkey.
    Search for articles by this author
  • Daver Yeker
    Affiliations
    Department of Paediatric Surgery, Cerrahpasa Medical Faculty, University of İstanbul, İstanbul, Turkey

    Department of Pathology, Cerrahpasa Medical Faculty, University of İstanbul, İstanbul, Turkey.
    Search for articles by this author
      This paper is only available as a PDF. To read, Please Download here.

      Abstract

      Congenital short bowel with functional intestinal obstruction and absence of appendix vermiformis is a very rare condition with poor prognosis. Seventeen cases of congenital short bowel have been reported previously in the literature. The etiology is unknown. In this report, a case of congenital short bowel, combined with functional intestinal obstruction, malrotation, and absence of the appendix vermiformis, is presented and the pathogenesis discussed.

      Keywords

      To read this article in full you will need to make a payment

      Purchase one-time access:

      Academic & Personal: 24 hour online accessCorporate R&D Professionals: 24 hour online access
      One-time access price info
      • For academic or personal research use, select 'Academic and Personal'
      • For corporate R&D use, select 'Corporate R&D Professionals'

      Subscribe:

      Subscribe to Journal of Pediatric Surgery
      Already a print subscriber? Claim online access
      Already an online subscriber? Sign in
      Institutional Access: Sign in to ScienceDirect

      References

        • Hamilton JR
        • Reilly BJ
        • Morecki R
        Short small intestine associated with malrotation: A newly described congenital cause of intestinal malabsorbtion.
        Gastroenterology. 1969; 56: 124-136
        • Kern IB
        • Harris MJ
        Congenital short bowel.
        Aust N Z J Surg. 1973; 42: 283-287
        • Senocak ME
        • Buyukpamukcu N
        • Hicsonmez A
        Ileal atresia due to intrauterine intussusception caused by Meckel's diverticulum.
        Pediatr Surg Int. 1990; 5: 64-66
        • Dorney SF
        • Byre WJ
        • Ament ME
        Case of congenital short intestine: Survival with use of long term parenteral feeding.
        Pediatrics. 1986; 77: 386-389
        • Adejuyigbe O
        • Odesanmi WO
        Intrauterine intussusception causing intestinal atresia.
        J Pediatr Surg. 1990; 5: 562-563
        • Das PC
        • Radhakrishna K
        • Rao PLNG
        Intrauterine intussusception as a cause of intestinal atresia.
        Indian Pediatrics. 1992; 29: 1139-1141
        • Grosfeld JI
        • Clathworthy HW
        The nature of Ileal atresia due to intrauterine intussusception.
        Arch Surg. 1970; 100: 714-717
        • Todani T
        • Tabuchi K
        • Tanaka S
        Intestinal atresia due to intrauterine intussusception: Analysis of 24 cases in Japan.
        J Pediatr Surg. 1975; 10: 445-451
        • Gündogdu Z
        • Senocak ME
        Intrauterine intussusception due to Meckel's diverticulum as a cause of ileal atresia: Analysis of 2 cases.
        Eur J Pediatr Surg. 1996; 6: 52-54
        • Louw JH
        Congenital intestinal atresia and severe stenosis in the newborn: Report of 79 cases.
        South Afr Clin Sci. 1952; 3: 109-129
        • Louw JH
        The natural cure of an acute intussusception.
        The Practitioner. 1949; 163: 233-235
        • Robb WAT
        • Souter W
        Spontaneous sloughing and healing of intussusception: Historical review and report of a case.
        Br J Surg. 1962; 49: 542-544
        • Shawis RN
        • Rangecroft L
        • Cook RCM
        • et al.
        Functional intestinal obstruction associated with malrotation and short small bowel.
        Jour Pediatr Surg. 1984; 19: 172-173
        • Huysman WA
        • Tibboel D
        • Bergmeijer JH
        • et al.
        Long-term survival of a patient with congenital short bowel and malrotation.
        J Pediatr Surg. 1991; 26: 103-105
        • Wu TJ
        • Teng RJ
        • Cheng MH
        • Cphen CC
        Congenital short bowel syndrome. Report of a case treated with home central parenteral nutrition.
        J Formasan Med Assoc. 1992; 91: 470-472